Primitive neuroectodermal tumor

Primitive neuroectodermal tumor is a malignant (cancerous) neural crest tumor. It is a rare tumor, usually occurring in children and young adults under 25 years of age. The overall 5 year survival rate is about 53%.

Not to be confused with pancreatic neuroendocrine tumor, which is also abbreviated as PNET.
Primitive neuroectodermal tumor
Other namesPNET
Micrograph of an H&E stained section of a peripheral PNET.
SpecialtyOncology

It gets its name because the majority of the cells in the tumor are derived from neuroectoderm, but have not developed and differentiated in the way a normal neuron would, and so the cells appear "primitive". PNET belongs to the Ewing family of tumors.

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